Nadir M. Maraldi

Overview

Best Publications

• Autophagy is defective in collagen VI muscular dystrophies, and its reactivation rescues myofiber degeneration

  Paolo Grumati;Luisa Coletto;Patrizia Sabatelli;Matilde Cescon

  565
  Citations

• Altered pre-lamin A processing is a common mechanism leading to lipodystrophy

  Cristina Capanni;Elisabetta Mattioli;Marta Columbaro;Enrico Lucarelli

  260
  Citations

• Cyclosporin A corrects mitochondrial dysfunction and muscle apoptosis in patients with collagen VI myopathies

  Luciano Merlini;Alessia Angelin;Tania Tiepolo;Paola Braghetta

  249
  Citations

• Regulation of novel protein kinase C ε by phosphorylation

  Vittoria Cenni;Heike Döppler;Erica D. Sonnenburg;Nadir Maraldi

  227
  Citations

• Mitochondrial dysfunction in the pathogenesis of Ullrich congenital muscular dystrophy and prospective therapy with cyclosporins

  Alessia Angelin;Tania Tiepolo;Patrizia Sabatelli;Paolo Grumati

  223
  Citations

• Rescue of heterochromatin organization in Hutchinson-Gilford progeria by drug treatment

  M. Columbaro;C. Capanni;E. Mattioli;G. Novelli

  187
  Citations

• Cellular and molecular events during chondrogenesis of human mesenchymal stromal cells grown in a three-dimensional hyaluronan based scaffold.

  Gina Lisignoli;Sandra Cristino;Anna Piacentini;Stefania Toneguzzi

  172
  Citations

• Ataxin-3 is Transported Into the Nucleus and Associates with the Nuclear Matrix

  Danilo Tait;Massimo Riccio;Annie Sittler;Eberhard Scherzinger

  167
  Citations

• Mutations in the retinoblastoma-related gene RB2/p130 in lung tumors and suppression of tumor growth in vivo by retrovirus-mediated gene transfer.

  Pier Paolo Claudio;Candace M. Howard;Candace M. Howard;Carmen Pacilio;Carmen Pacilio;Caterina Cinti

  166
  Citations

• Heart-Specific Localization of Emerin: New Insights Into Emery-Dreifuss Muscular Dystrophy

  Luca Cartegni;Marina Raffaele di Barletta;Rita Barresi;Stefano Squarzoni

  163
  Citations

• Collagen VI deficiency affects the organization of fibronectin in the extracellular matrix of cultured fibroblasts.

  Patrizia Sabatelli;Paolo Bonaldo;Giovanna Lattanzi;Paola Braghetta

  147
  Citations

• Genetic ablation of cyclophilin D rescues mitochondrial defects and prevents muscle apoptosis in collagen VI myopathic mice

  Elena Palma;Tania Tiepolo;Alessia Angelin;Patrizia Sabatelli

  143
  Citations

• Alterations of nuclear envelope and chromatin organization in mandibuloacral dysplasia, a rare form of laminopathy.

  Ilaria Filesi;Francesca Gullotta;Giovanna Lattanzi;Maria Rosaria D'Apice

  139
  Citations

• Laminopathies and lamin‐associated signaling pathways

  Nadir M. Maraldi;Cristina Capanni;Vittoria Cenni;Milena Fini

  131
  Citations

• Phospholipid interactions in rat liver nuclear matrix

  Lucio Cocco;Nadir M. Maraldi;Francesco A. Manzoli;R. Stewart Gilmour

  124
  Citations

• Association of emerin with nuclear and cytoplasmic actin is regulated in differentiating myoblasts.

  Giovanna Lattanzi;Vittoria Cenni;Sandra Marmiroli;Cristina Capanni

  116
  Citations

• Failure of lamin A/C to functionally assemble in R482L mutated familial partial lipodystrophy fibroblasts: altered intermolecular interaction with emerin and implications for gene transcription.

  Cristina Capanni;Vittoria Cenni;Elisabetta Mattioli;Patrizia Sabatelli

  111
  Citations

• Genetic alterations disrupting the nuclear localization of the retinoblastoma-related gene RB2/p130 in human tumor cell lines and primary tumors.

  Caterina Cinti;Pier Paolo Claudio;Candace M. Howard;Luca Maria Neri

  108
  Citations

• Genetic alterations of the retinoblastoma-related gene RB2/p130 identify different pathogenetic mechanisms in and among Burkitt's lymphoma subtypes.

  Caterina Cinti;Lorenzo Leoncini;Aggrey Nyongo;Filomena Ferrari

  108
  Citations

• Autophagic degradation of farnesylated prelamin A as a therapeutic approach to lamin-linked progeria

  V. Cenni;C. Capanni;M. Columbaro;M. Ortolani

  108
  Citations