Horst von Bernuth

Overview

Best Publications

• TLR3 deficiency in patients with herpes simplex encephalitis.

  Shen Ying Zhang;Shen Ying Zhang;Emmanuelle Jouanguy;Emmanuelle Jouanguy;Sophie Ugolini;Asma Smahi

  1319
  Citations

• Pyogenic Bacterial Infections in Humans with MyD88 Deficiency

  Horst Von Bernuth;Capucine Picard;Capucine Picard;Zhongbo Jin;Rungnapa Pankla;Rungnapa Pankla

  1249
  Citations

• The EUROclass trial: defining subgroups in common variable immunodeficiency

  Claudia Wehr;Teemu Kivioja;Christian Schmitt;Berne Ferry

  979
  Citations

• Diverse stimuli engage different neutrophil extracellular trap pathways

  Elaine F Kenny;Alf Herzig;Renate Krüger;Aaron Muth

  800
  Citations

• Neutrophils: Between host defence, immune modulation, and tissue injury

  Philipp Kruger;Mona Saffarzadeh;Alexander N. R. Weber;Nikolaus Rieber

  783
  Citations

• Autoantibodies neutralizing type I IFNs are present in ~ 4% of uninfected individuals over 70 years old and account for ~ 20% of COVID-19 deaths.

  Paul Bastard;Adrian Gervais;Adrian Gervais;Tom Le Voyer;Tom Le Voyer;Jérémie Rosain;Jérémie Rosain

  592
  Citations

• Human genetic and immunological determinants of critical COVID-19 pneumonia

  Unknown

  588
  Citations

• Mutations in STAT3 and IL12RB1 impair the development of human IL-17–producing T cells

  Ludovic de Beaucoudrey;Ludovic de Beaucoudrey;Anne Puel;Anne Puel;Orchidée Filipe-Santos;Orchidée Filipe-Santos;Aurélie Cobat;Aurélie Cobat

  496
  Citations

• Clinical Features and Outcome of Patients With IRAK-4 and MyD88 Deficiency

  Capucine Picard;Capucine Picard;Horst Von Bernuth;Horst Von Bernuth;Horst Von Bernuth;Pegah Ghandil;Pegah Ghandil;Pegah Ghandil;Maya Chrabieh;Maya Chrabieh

  488
  Citations

• Selective predisposition to bacterial infections in IRAK-4–deficient children: IRAK-4–dependent TLRs are otherwise redundant in protective immunity

  Cheng Lung Ku;Horst Von Bernuth;Horst Von Bernuth;Capucine Picard;Shen Ying Zhang

  470
  Citations

• Human TLR-7-, -8-, and -9-Mediated Induction of IFN-α/β and -λ Is IRAK-4 Dependent and Redundant for Protective Immunity to Viruses

  Kun Yang;Kun Yang;Anne Puel;Shenying Zhang;Shenying Zhang;Céline Eidenschenk

  356
  Citations

• X-linked susceptibility to mycobacteria is caused by mutations in NEMO impairing CD40-dependent IL-12 production

  Orchidée Filipe-Santos;Jacinta Bustamante;Margje H. Haverkamp;Margje H. Haverkamp;Emilie Vinolo

  309
  Citations

• IRAK-4-and MyD88-Dependent Pathways Are Essential for the Removal of Developing Autoreactive B Cells in Humans

  Isabelle Isnardi;Yen Shing Ng;Iva Srdanovic;Roja Motaghedi

  263
  Citations

• A Global Effort to Define the Human Genetics of Protective Immunity to SARS-CoV-2 Infection.

  Jean-Laurent Casanova;Helen C. Su;Covid Human Genetic Effort

  230
  Citations

• Experimental and natural infections in MyD88- and IRAK-4-deficient mice and humans.

  Horst von Bernuth;Horst von Bernuth;Capucine Picard;Capucine Picard;Anne Puel;Anne Puel;Jean-Laurent Casanova

  220
  Citations

• Mutations in AP3D1 associated with immunodeficiency and seizures define a new type of Hermansky-Pudlak syndrome.

  Sandra Ammann;Sandra Ammann;Ansgar Schulz;Ingeborg Krägeloh-Mann;Nele M. G. Dieckmann

  203
  Citations

• Human Toll-like receptor-dependent induction of interferons in protective immunity to viruses.

  Shen-Ying Zhang;Emmanuelle Jouanguy;Emmanuelle Jouanguy;Vanessa Sancho-Shimizu;Horst von Bernuth

  199
  Citations

• IRAK4 and NEMO mutations in otherwise healthy children with recurrent invasive pneumococcal disease

  Cheng Lung Ku;Capucine Picard;Melinda Erdõs;Axel Jeurissen

  189
  Citations

• Initial presenting manifestations in 16,486 patients with inborn errors of immunity include infections and noninfectious manifestations.

  Julian Thalhammer;Gerhard Kindle;Alexandra Nieters;Stephan Rusch

  158
  Citations

• Inherited disorders of human Toll-like receptor signaling: immunological implications.

  Cheng‐Lung Ku;Kun Yang;Jacinta Bustamante;Anne Puel

  158
  Citations

• Inborn errors in RNA polymerase III underlie severe varicella zoster virus infections

  Benson Ogunjimi;Shen-Ying Zhang;Katrine Biehl Sørensen;Kristian A Skipper

  146
  Citations

• The expansion of human T-bet high CD21 low B cells is T cell dependent

  Baerbel Keller;Valentina Strohmeier;Valentina Strohmeier;Ina Harder;Susanne Unger

  134
  Citations