Arnold W. Strauss

Overview

Best Publications

• Tandem mass spectrometric analysis for amino, organic, and fatty acid disorders in newborn dried blood spots: a two-year summary from the New England Newborn Screening Program.

  Thomas H. Zytkovicz;Eileen F. Fitzgerald;Deborah Marsden;Cecilia A. Larson

  697
  Citations

• Newborn Screening: Toward a Uniform Screening Panel and System—Executive Summary

  Michael S. Watson;Marie Y. Mann;Michele A. Lloyd-Puryear;Piero Rinaldo

  597
  Citations

• The nucleotide sequence of rat liver fatty acid binding protein mRNA.

  J I Gordon;D H Alpers;R K Ockner;A W Strauss

  316
  Citations

• Cardiac and Skeletal Muscle Defects in a Mouse Model of Human Barth Syndrome

  Devrim Acehan;Frederic Vaz;Riekelt H. Houtkooper;Jeanne James

  279
  Citations

• The molecular basis of pediatric long chain 3-hydroxyacyl-CoA dehydrogenase deficiency associated with maternal acute fatty liver of pregnancy

  Harold F. Sims;Jeffrey C. Brackett;Cynthia K. Powell;William R. Treem

  273
  Citations

• Cloning of a cDNA encoding rat intestinal fatty acid binding protein

  David H. Alpers;Arnold W. Strauss;Robert K. Ockner;Nathan M. Bass

  245
  Citations

• Dilated cardiomyopathy in infants and children.

  Michael L Griffin;Antonio Hernandez;Thomas C Martin;David Goldring

  238
  Citations

• Proteolytic processing of human preproapolipoprotein A-I. A proposed defect in the conversion of pro A-I to A-I in Tangier's disease.

  J I Gordon;H F Sims;S R Lentz;C Edelstein

  230
  Citations

• Molecular basis of human mitochondrial very-long-chain acyl-CoA dehydrogenase deficiency causing cardiomyopathy and sudden death in childhood.

  Arnold W. Strauss;Cynthia K. Powell;Daniel E. Hale;Melissa M. Anderson

  229
  Citations

• The primary translation product of rat intestinal apolipoprotein A-I mRNA is an unusual preproprotein.

  J I Gordon;D P Smith;R Andy;D H Alpers

  222
  Citations

• Medium chain acyl-CoA dehydrogenase deficiency in Pennsylvania: neonatal screening shows high incidence and unexpected mutation frequencies

  Rana Ziadeh;Eric P Hoffman;David N Finegold;Rita C Hoop

  213
  Citations

• Cloning and characterization of human pancreatic lipase cDNA.

  M E Lowe;J L Rosenblum;A W Strauss

  209
  Citations

• Lack of mitochondrial trifunctional protein in mice causes neonatal hypoglycemia and sudden death

  Jamal A. Ibdah;Hyacinth Paul;Yiwen Zhao;Scott Binford

  202
  Citations

• Human placenta metabolizes fatty acids: implications for fetal fatty acid oxidation disorders and maternal liver diseases

  Prem S. Shekhawat;Michael J. Bennett;Yoel Sadovsky;D. Michael Nelson

  199
  Citations

• Molecular Heterogeneity in Very-Long-Chain Acyl-CoA Dehydrogenase Deficiency Causing Pediatric Cardiomyopathy and Sudden Death

  Amit Mathur;Harold F. Sims;Deepika Gopalakrishnan;Beverly Gibson

  199
  Citations

• Toward a Molecular Understanding of Congenital Heart Disease

  R. M. Payne;Mark Johnson;J. W. Grant;A. W. Strauss

  191
  Citations

• The tissue-specific expression and developmental regulation of two nuclear genes encoding rat mitochondrial proteins. Medium chain acyl-CoA dehydrogenase and mitochondrial malate dehydrogenase.

  D P Kelly;J I Gordon;R Alpers;A W Strauss

  177
  Citations

• Mechanism of hyperinsulinism in short-chain 3-hydroxyacyl-CoA dehydrogenase deficiency involves activation of glutamate dehydrogenase

  Changhong Li;Pan Chen;Andrew Palladino;Srinivas Narayan

  175
  Citations

• Improved outcomes of pediatric dilated cardiomyopathy with utilization of heart transplantation.

  Anna E. Tsirka;Kathryn Trinkaus;Su Chiung Chen;Steven E. Lipshultz

  163
  Citations

• A Delphi clinical practice protocol for the management of very long chain acyl-CoA dehydrogenase deficiency

  Georgianne L. Arnold;Johan Van Hove;Debra Freedenberg;Arnold Strauss

  163
  Citations